Abstract. ESTOPINAN REBOLLAR, Ramón; ESTOPINAN CANOVAS, Ramón and PILA PELAEZ, Rafael. Enfermedad de Hirschsprung en un adulto. Rev Col. Resumen. LOMBANA, Luis Jorge y DOMINGUEZ, Luis Carlos. Surgery in adult Hirschsprung’s disease. Rev Col Gastroenterol [online]. , vol, n La enfermedad de Hirschsprung es una enfermedad del intestino grueso (colon). Normalmente, las heces fecales son empujadas a través del colon por.

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No abnormalities resulted from the rectal examination. A midline laparotomy was performed, finding a massive dilatation of sigmoid colon, attaining a diameter of 44 cm at its more dilated portion. The diagnosis is made by barium enema, anorectal manometry and rectal biopsy.

Hirschsprung disease is certainly diagnosed after birth. The girl refers onset of fecal incontinence at the age of Hirschsprung’s disease was described inwith the report of 20 cases of congenital megacolon in children.

Given these findings, emergency surgery was decided. There are few reports on this disease in stages after infancy in the national and international literature. Surgical treatment for the disease was described in This item has received.

Niger J Clin Pract ; This factor contributed to the delay in her diagnosis, driving the pediatrician out of a HD hypothesis. Rev Col Gastroenterol, 31pp. In recent years, the Duhamel technique has been considered as the best option. Several procedures are used to manage this disease after hirschspruny currently the option of choice is the surgical procedure of Duhamel.


Vólvulo en adultos | HCA Healthcare

The primary defect is absence of ganglion cells in Meiss-ner plexus submucosal and Auerbach plexus myenteric in the affected segment of large bowel.

Complaints of fecal incontinence are often reported in the literature in cases enfermeddad functional constipation and of idiopathic megacolon. Informe de um caso. Hirschsprung’s disease HD is a malformation of the large intestine characterized by the absence of ganglion cells in submucosal and myenteric plexus, which produces a functional obstruction and dilatation proximal to the affected segment 1.

It is a rare disease in adulthood, but its diagnosis should be considered in cases of constipation that is refractory to conventional medical therapy.

Peritoneal irritation was not found. SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s hirschsprumg. In the pediatric population a constipation history since the first month of life, the delay on the elimination of meconium beyond the 24 hours, abdominal distension is a suspicion of Congenital Megacolon.

Some patients reach adulthood without a diagnosis for this disease. Biopsies of the rectum.


Later, a barium enema Fig. We include a review of existing literature. IHC x positive for S in the nerve plexuses.

Vólvulo en adultos

J Pediatr Rio de J. It is important to consider the presence of this rare pathologic process in young adult patients with treatment-refractory chronic constipation, in whom other more common diseases have been ruled out through easily accessed studies, such as imaging or anorectal physiology studies. Previous history of xdultos operated inintestinal resection in childhood unknown etiologychronic constipation, smoker of 20 cigarettes per day and moderate drinker.

A CT scan was performed, showing a massive dilatation of sigmoid colon, which compresses liver to the right upper quadrant, stomach into the left upper quadrant and bowel loops into the right flank Figs. Enfermedad de Hirschsprung en el adulto.

Physical examination revealed a mildly distended abdomen and no other relevant alterations. Therefore, the most liquid stools upstream pass around the fecal impaction and produce the reported symptom, known as fecal incontinence soiling.